BACKGROUND & AIMS:
:Proliferating trichilemmal tumor (PTT) is a rare but morphologically distinct tumor that usually arises on the scalp of elderly women. It is composed of multiple cysts consisting of squamous epithelium with trichilemmal keratinization without granular layer interposition. Vulvar proliferating trichilemmal cyst is very rare, with, to the best of our knowledge, only 3 cases previously reported in the literature. We describe a 39-year-old woman with recurrent PTT on the left labium majus of the vulva, which had been excised from the same side 5 years before. She had a palpable nodule, approximately 2 cm in size, which was firm, mobile, and nontender; without erythema and ulceration; and covered by normal skin on the vulva. There was no inguinal lymphadenopathy. The lesion was removed by wide surgical excision; because of the tissue elasticity, primary closure was possible. The pathology result was reported as proliferating trichilemmal carcinoma with tumor-free margins. Although local recurrence after wide excision is rare, we recommend complete excision for treatment of PTT and long-term follow-up because of the possibility of recurrence.
背景与目标:
增生性毛囊瘤 (PTT) 是一种罕见但形态上不同的肿瘤,通常发生在老年妇女的头皮上。它由多个囊肿组成,由鳞状上皮组成,具有三鞘角化,没有颗粒层插入。外阴增生的毛囊囊肿非常罕见,据我们所知,以前文献中仅报道了3例。我们描述了一名39岁的女性,在外阴的左阴唇上复发性PTT,该女性在5年前从同一侧切除。她有一个可触及的结节,大小约2厘米,坚硬,可移动且不触痛; 没有红斑和溃疡; 外阴被正常皮肤覆盖。无腹股沟淋巴结肿大。通过广泛的手术切除切除病变; 由于组织弹性,可以进行一次闭合。病理结果报告为增殖性毛囊癌,边缘无瘤。尽管广泛切除后的局部复发很少见,但由于复发的可能性,我们建议完全切除治疗PTT并进行长期随访。